Abstract:
Dyke-Davidoff Masson syndrome (DDMS) was first reported as rare congenital malformation in 1933 by Dyke. The classical clinical presentation includes facial asymmetry, contralateral hemiplegia or hemiparesis and seizures. The clinical findings may be of variable degree according to the extent of the brain injury. Computure tomography and magnetic resonance imaging are the procedures of choice with respect to assesment of the etiology and extent cerebral parenchymal involvoment in DDMS. Atrophy of the cerebral hemisphere with ipsilateral shift of the ventricles, dilate lateral ventricle, cerebellar atrophy, prominent cortical sulci, calvarial thickening, enlargement of mastoid air cells and paranasal sinuses and elevated temporal bone are well-known radiological findings of DDMS. We reported the case of DDMS with clinical and radiological findings.